Diffuse cutaneous systemic sclerosis: A case report
International Journal of Development Research
Diffuse cutaneous systemic sclerosis: A case report
Received 20th January, 2018, Received in revised form, 17th February, 2018, Accepted 18th March, 2018, Published online 30th April, 2018
Copyright © 2018, Safura Sultana et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
Systemic sclerosis (SSc, Scleroderma) is a rare connective tissue disorder that is highly diverse in its multisystem clinical presentation and follows a variable course. Systemic sclerosis is a disease that will lead to collagen diposition and fibrosis of skin and various internal organs like lungs, kidneys, blood vessels, and gastrointestinal tract. Systemic sclerosis can be clinically discerned into two subsets based on skin findings and serological data they are limited cutaneous systemic sclerosis (lSSc) and diffuse cutaneous systemic sclerosis (DcSSc). Diffuse cutaneous systemic sclerosis is governed by rapid progressive fibrosis of skin and other internal organs. Diffuse cutaneous systemic sclerosis is characterised by proximal skin sclerosis, Raynauds phenomenon, sclerodactyly, degenarative changes and vascular abnormalities. This case reports presents a case of diffuse cutaneous systemic sclerosis in 45yr old female patient with characteristic systemic and intraoral manifestations.
